Comparison | Parameter | Group1 | Group2 | p-value |
---|---|---|---|---|
1 | Condition | CF (n = 9) | Healthy controls (n = 3) | NA |
Age in years, median (IQR) | 7 (6, 18) | 8 (8, 8) | NS | |
Gender: Male, n (%) | 3 (33.3%) | 1 (33.3%) | NS | |
2 | CF Phenotype | Severe1 (n = 6) | Mild2 (n = 3) | NA |
Age in years, median (IQR) | 10 (7, 25) | 6 (5, 7) | NS | |
Gender: Male, n (%) | 3 (33.3%) | 1 (33.3%) | NS | |
Gender: Male, n (%) | 2 (33.3%) | 1 (33.3%) | NS | |
Sweat chloride, median (IQR) | 105 (100, 123) | 67 (30, 77) | 0.007* | |
Mucoid P. aeruginosa, n (%) | 4 (66.7%) | 0 | NS | |
FEV1% predicted, median (IQR) | 103 (85, 113) | 113 (110, 118) | NS | |
F508del homozygotes, n (%) | 6 (66.7%) | 0 | 0.01†|