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Table 3 Comparison of therapies and complications of 3 patients with GSD type Ib

From: Clinical analysis and long-term treatment monitoring of 3 patients with glycogen storage disease type Ib

  Patient 1 Patient 2 Patient 3
Clinical diagnosis Genetic diagnosis Last visit Clinical diagnosis Genetic diagnosis Last visit Clinical diagnosis Genetic diagnosis Last visit
Therapies          
 Uncooked cornstarch Irregular Irregular Regular Regular Regular Regular
 Neutropenia treatment No Yes G-CSF No Yes Yes No Yes Yes
 Sodium Bicarbonate Tablets No Yes Yes No Yes No No No No
Complications          
 Number of hospitalizations (times/year) 1 0.36 3 1 0 0 1 0 0
 Inflammatory bowel disease No No Yes No No No No No No
 Mouth ulcers Yes Yes Yes Usually Occasionally Decrease Occasionally No No
 Upper respiratory tract infection Yes Yes Yes Yes Less Less Repeatedly Occasionally Decrease
 Pancreatitis No No Yes No No No No No No
 Other Chronic superficial gastritis