Previous publications | Age at SNHL onset (years) | Interventions |
---|---|---|
Shastry et al. [1], patient 100.3 | 18 | NA |
Shastry et al. [1], patient 200.5 | 15 | NA |
Shastry et al. [1], patient 300.4 | 7 | NA |
Shastry et al.[1], patient 400.3 | 8 | NA |
Shastry et al. [1], patient 500.4 | 16 | NA |
Shastry et al. [1], patient 600.4 | 14 | NA |
Shastry et al. [1], patient 700.3 | 6 | NA |
Weedon et al. [2], patient 1 | 12 | Bilateral hearing aids |
Weedon et al. [17], patient 2 | 33 | NA |
Pelosini et al. [9] | 25 | Hearing aid |
Reinier et al. [10] | 10 | NA |
Lessel et al. [3], patient 1 | N | NA |
Lessel et al. [3], patient 2 | 12 | NA |
Lessel et al. [3], patient 3 | 11 | NA |
Lessel et al. [3], patient 4 | N | NA |
Lessel et al. [3], patient 5 | 14 | NA |
Lessel et al. [3], patient 6 | 14 | NA |
Lessel et al. [3], patient 7 | N | NA |
Lessel et al. [3], patient 8 | NA | NA |
Ajluni et al. [18], patient 6 | N | N |
Ajluni et al. [18], patient 7 | N | N |
Elouej et al. [7], patient 1 | N | N |
Elouej et al. [7], patient 2 | 4 | Bilateral hearing aids |
Okada et al. [11] | 7 | Hearing aids |
Wang et al. [12] | 10 | Hearing aids |
Fiorillo et al. [13] | 2 | NA |
Sasaki et al. [14] | Puberty | NA |
Wang et al. [15] | 15 | NA |
Oh et al. [8], SB127-219 | NA | NA |
Oh et al. [8], SB127-277 | NA | NA |
Yu et al. [16] | 25 | NA |
Zhou et al. [17] | 20 | NA |
Murdocca et al. [6] | NA | NA |
This study proband | 6 | Bilateral hearing aids |