Fig. 1

Histopathological characterization of the patient’s lungs. a Pulmonary hypoplasia; bronchus with cartilage is very close to the pleura, hematoxylin and eosin, (H&E), 4x. b Interlobular septum with dilated lymphatics and normally placed vein. Pulmonary arterioles are thickened. The respiratory bronchiole is too close to the septum, consistent with hypoplasia. H&E, 10x. c Mild growth disturbance with enlarged simplified alveoli, with normal capillaries